Cystic Fibrosis

Cystic fibrosis (CF) is an inherited disorder of mucus and sweat glands. It mainly affects your lungs, pancreas, liver, intestines, paranasal sinuses and genitals. CF will thicken your mucus. Mucus clogs the lungs and causes respiratory disturbances that easily propagate bacteria. This can lead to repeated pulmonary infections and lung injuries

CF symptoms and severity vary. Some people have serious problems since birth. Some people are younger or younger, depending on a lighter illness. Sometimes you will have some symptoms, but later you may have more symptoms

CF is diagnosed by various examinations such as genetic testing, blood test, sweat examination. There is no cure for CF, but in recent years the treatment has been greatly improved. In the past, most of the causes of CF death were children and adolescents. Today, some people with CF live in their 40s, 50s or more by improving their treatment. The treatment includes chest physical therapy, nutritional therapy and respiratory therapy, medicine and exercise.

Recent advances in cystic fibrosis management have greatly improved the prognosis. More than 90% of children diagnosed with cystic fibrosis will live in their teenage. The average survival age of children born after 1990 is presumed to be 40 years old. This can be further improved by gene therapy technology in the future.

Cystic fibrosis is an autosomal recessive disorder - that is, two defective genes (one for each parent) are needed to develop the disease. The gene thought to cause cystic fibrosis is called cystic fibrosis transmembrane conductance regulator or CFTR. This gene is on chromosome 7. The severity and extent of this disease vary greatly among patients with cystic fibrosis. Typically, this condition results in chloride transport defects through epithelial cells and an increase in the viscosity of bodily secretions, particularly from the respiratory tract (ie, lungs, throat) and pancreas. As a result, the patient is prone to pancreatic dysfunction and recurrent thoracic infection

Marten deVlieger was initially diagnosed with cystic fibrosis. This is a degenerative incurable disease affecting the whole body, especially the lungs. "Life with cystic fibrosis is a continuous task." Most of us are said to be unable to live at 2, 10, 21 from birth. It is rare that people live in today's average CF life, he said he believes that 'this might be me'. But Marten dreams of independence. Since he wanted to take a helicopter, he used it as a teenager to locate local waste dumps, find metal scraps and parts and reflect the traditional mucus relaxation method of CF patients. . His first iteration was too much trouble to hurt him. However, ChestMaster 5000 was born.